Hopkins’ syndrome

Hopkins’ syndrome

Authors

  • Maria Roberta Longo Dipartimento di Pediatria e Neurologia pediatrica, Azienda Ospedaliera Universitaria OVE-Policlinico, Università di Catania
  • Raffaele Falsaperla Dipartimento di Pediatria e Neurologia pediatrica, Azienda Ospedaliera Universitaria OVE-Policlinico, Università di Catania
  • Catia Romano Dipartimento di Pediatria e Neurologia pediatrica, Azienda Ospedaliera Universitaria OVE-Policlinico, Università di Catania
  • Eleonora Passaniti Dipartimento di Pediatria e Neurologia pediatrica, Azienda Ospedaliera Universitaria OVE-Policlinico, Università di Catania
  • Piero Pavone Dipartimento di Pediatria e Neurologia pediatrica, Azienda Ospedaliera Universitaria OVE-Policlinico, Università di Catania

DOI:

https://doi.org/10.7175/cmi.v5i2.508

Keywords:

Hopkins’ syndrome, Asthmatic amyotrophy, Asthma, Childhood

Abstract

Hopkins’ syndrome is a rare disease that affects the anterior horn of the spinal cord after an acute episode of asthma in children with atopic disease. A viral infection or immunological suppression in atopic subjects might be the cause of occurrence of this syndrome, although the mechanism due to the etiopathogenesis of the disease still remains unknown.In general, this disease is manifested by a few days to a few weeks after an acute asthma attack, with flaccid paralysis of one or more limbs and in some cases residual muscle atrophy. The response to corticosteroid therapy is good and rare the possibility of recurrence.

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Published

2011-06-15

Issue

Section

Case report
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